Arrhythmogenic Dystrophy of the Right Ventricle

Dystrophie Arythmogène du Ventricule Droit

Arrhythmogenic Dystrophy of the Right VentricleCLINICAL SIGNS:

* loss of consciousness in a young adult, with the effort.

* sudden death.

* notion of recent infectious episode.


* ECG :

– often normal.

– QRS elongation> 0.11 seconds in the right precords whereas on the other leads, the QRS is normal.

 (QRS duration in V1, V2 or V3 – duration in V6) greater than or equal to 25 ms.

– Incomplete limb block aspect right on precordial straight lines (epsilon wave: small ST segment deflection).

Negative wave T in V1, V2 sometimes from V1 to V6.

– Ventricular extrasystoles with left delay.

* rhythmic assessment because risk of sudden death by ventricular tachycardia.

* echocardiography, cardiac scintigraphy, cardiac magnetic resonance imaging.


* hospitalization if doubt diagnosis.

– Establishment of an implantable defibrillator.