* loss of consciousness in a young adult, most often a man: syncope.
* Sudden death by ventricular rhythm (FV, TV).
* notion of family history of sudden death, malaise in 60% of cases.
* ECG :
– often normal.
– right branch block with J point elevation.
– sometimes the ST segment offset in front.
* rhythmic assessment with stress test, test with Ajmaline or flecainide.
* hospitalization if doubt diagnosis.
– Establishment of an implantable defibrillator.